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. I have no financial disclosure.. Hemophilia . A rare X-linked inherited bleeding disorder Hemophilia A (factor VIII deficiency) - 1/10,000 live male birthsHemophilia B (factor IX deficiency) - 1/30,000 live male birthsThe severity of the disease is based on baseline factor VIII activityMild -
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1. Hemophilia A with inhibitors Tzu-Fei Wang
2/17/12
2. I have no financial disclosure.
3. Hemophilia A rare X-linked inherited bleeding disorder Hemophilia A (factor VIII deficiency) - 1/10,000 live male births Hemophilia B (factor IX deficiency) - 1/30,000 live male births The severity of the disease is based on baseline factor VIII activity Mild - >5% (36-44%) Moderate – 1-5% (17-19%) Severe - <1% (38-44%) A chronic, costly disease, and the best care is provided by comprehensive care centers. The development of factor VIII alloantiboby (inhibitors) is a dreaded consequence.